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01-06-2017 | Case report

Malignant Peripheral Nerve Sheath Tumour of the Small Bowel Presenting with Intussusception and Perforation: a Double Jeopardy?

Authors: Ananth P. Abraham, Joshua Franklyn, Jagan Chandramohan, Pranay Gaikwad, John C. Muthusami

Published in: Indian Journal of Surgical Oncology | Issue 2/2017

Abstract

Malignant peripheral nerve sheath tumours (MPNST) are rare soft tissue sarcomas which largely occur in the extremities and the head and neck region. The tumours are aggressive with a high rate of recurrence. Radical surgical resection remains the treatment of choice with adjuvant radiation therapy and chemotherapy still failing to demonstrate a clear benefit. The gastrointestinal tract is an exceedingly rare site for these tumours. We report an unusual case of a young male with an MPNST of the small bowel who presented with an ileocolic intussusception and sigmoid perforation.

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Title: Malignant Peripheral Nerve Sheath Tumour of the Small Bowel Presenting with Intussusception and Perforation: a Double Jeopardy?
Authors: Ananth P. Abraham
Joshua Franklyn
Jagan Chandramohan
Pranay Gaikwad
John C. Muthusami
Publication date: 01-06-2017
Publisher: Springer India
Published in: Indian Journal of Surgical Oncology / Issue 2/2017
Print ISSN: 0975-7651
Electronic ISSN: 0976-6952
DOI: https://doi.org/10.1007/s13193-016-0572-7

At a glance: The STEP trials

Springer Medicine

Malignant Peripheral Nerve Sheath Tumour of the Small Bowel Presenting with Intussusception and Perforation: a Double Jeopardy?

Abstract

At a glance: The STEP trials

Springer Medicine

Abstract

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