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BMC Musculoskeletal Disorders
Published in: BMC Musculoskeletal Disorders 1/2020

Open Access 01-12-2020 | Magnetic Resonance Imaging | Case report

Synovial sarcoma presenting as an intra-articular mass in a pediatric patient: a case report

Authors: Omar A. Al-Mohrej, Saeed A. Al-Jarallah, Hamad H. Al-Dakhil Allah, Rajeev Pant, Zayed S. Al-Zayed

Published in: BMC Musculoskeletal Disorders | Issue 1/2020

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Abstract

Background

Synovial sarcoma (SS) is one of the reported sarcomas in the pediatric and adult populations. Delay in diagnosis and treatment is common in SS cases. SS may be excised before the correct diagnosis is made.

Case presentation

we present a case involving a 4-year-old boy who visited our service with complaints of left knee pain and limited knee flexion. Initially, the child was diagnosed with osteochondromatosis. Surgical excision was opted, and initial histopathological examination revealed a fibrous histiocytoma. The slide and blocks were then brought to the King Faisal Specialist Hospital Research Center (KFSH&RC) and histopathologic analysis has shown a well-circumscribed nodule in the synovium with a sub-synovial monomorphic spindle cell sarcoma, confirmed by fluorescence in situ hybridization (FISH).

Conclusions

Therefore, we strongly recommend considering all differential diagnoses for soft-tissue masses when planning surgical management.
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Metadata
Title
Synovial sarcoma presenting as an intra-articular mass in a pediatric patient: a case report
Authors
Omar A. Al-Mohrej
Saeed A. Al-Jarallah
Hamad H. Al-Dakhil Allah
Rajeev Pant
Zayed S. Al-Zayed
Publication date
01-12-2020
Publisher
BioMed Central
Published in
BMC Musculoskeletal Disorders / Issue 1/2020
Electronic ISSN: 1471-2474
DOI
https://doi.org/10.1186/s12891-020-03312-3

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