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Published in: Child's Nervous System 5/2019

01-05-2019 | Magnetic Resonance Imaging | Case Report

A case of focal cortical dysplasia type Ib atypically showing reversible intensity changes on magnetic resonance imaging which could be affected by epileptic discharge activity

Authors: Naoto Kuroda, Ayataka Fujimoto, Hideo Enoki, Yoshifumi Arai, Tohru Okanishi

Published in: Child's Nervous System | Issue 5/2019

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Abstract

Focal cortical dysplasia (FCD) was first described as a distinct neuropathological entity in 1971 by Taylor and colleagues. FCD is thought to be an embryological migration disorder and is thus considered a non-progressive, unchangeable disease throughout life. A 9-year-old right-handed boy was referred from a local hospital for medically intractable epileptic seizures. Serial magnetic resonance images (MRI) showed intensity changes that indicated exacerbation and remission. After presurgical evaluations including intracranial video-electroencephalogram monitoring, we performed a lesionectomy aided by MRI and epileptic focus resection. He has been free from seizures for more than 3 years. Neuropathological findings showed FCD type Ib. We surgically treated a patient with FCD, which showed MRI intensity changes indicating exacerbation and remission. Although FCD type Ib is generally invisible on MRI, in this patient, changes in intensity on MRI made FCD type Ib visible.
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Metadata
Title
A case of focal cortical dysplasia type Ib atypically showing reversible intensity changes on magnetic resonance imaging which could be affected by epileptic discharge activity
Authors
Naoto Kuroda
Ayataka Fujimoto
Hideo Enoki
Yoshifumi Arai
Tohru Okanishi
Publication date
01-05-2019
Publisher
Springer Berlin Heidelberg
Published in
Child's Nervous System / Issue 5/2019
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI
https://doi.org/10.1007/s00381-019-04093-4

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