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Journal of Cardiothoracic Surgery

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01-12-2020 | Liposuction | Case report

Madelung’s disease and pulmonary aspergillosis: a case report and literature review

Authors: Weijiang Ma, Xilong Zhao, Xu Li, Chenxi Zang, Limin Yang, Yan Wang, Xin Liu

Published in: Journal of Cardiothoracic Surgery | Issue 1/2020

Abstract

Background

Madelung’s disease (MD) is a rare disorder of fat metabolism, which is usually associated with diabetes, hyperuricemia, liver disease, nevertheless there is no report of a patient with MD and pulmonary aspergillosis (PA). This article aimed to enhance the awareness of this two diseases and discuss the possible mechanism of the combination of them preliminarily.

Case presentation

In this case, we described a 56-year-old male patient with cough, expectoration and dyspnea. His neck has a very peculiar appearance. Chest enhanced CT scan showed there were multiple nodules in both lungs, some of which had cavities and the mediastinal lymph nodes were swollen. Ultrasound scan of the neck showed diffuse hyperplasia of subcutaneous fat in neck and bilateral supraclavicular fossa. Fortunately, after performing pulmonary wedge resection aimed at pathological examination and giving relevant treatments, this patient was finally diagnosed as MD with PA, and his symptoms were significantly relieved.

Conclusions

MD is rare, the phenomenon that MD combined with PA is rarer. Immune disorder may be the possible mechanism.

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Title: Madelung’s disease and pulmonary aspergillosis: a case report and literature review
Authors: Weijiang Ma
Xilong Zhao
Xu Li
Chenxi Zang
Limin Yang
Yan Wang
Xin Liu
Publication date: 01-12-2020
Publisher: BioMed Central
Keywords: Liposuction
Liposuction
Dyspnea
Aspergillosis
Dyspnea
Liposuction
Published in: Journal of Cardiothoracic Surgery / Issue 1/2020
Electronic ISSN: 1749-8090
DOI: https://doi.org/10.1186/s13019-020-01166-3

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Madelung’s disease and pulmonary aspergillosis: a case report and literature review

Abstract

Background

Case presentation

Conclusions

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Background

Case presentation

Conclusions

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