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01-12-2019 | Liposarcoma | Case Report

Paraneoplastic Syndrome Associated with the Retroperitoneal Dedifferentiated Liposarcoma: an Atypical Presentation and Review of the Literature

Authors: Jeewan Ram Vishnoi, Ankit Jain, Sanjeev Misra, Puneet Pareek, Meenakshi Rao, Binit Sureka, Ashok Puranik

Published in: Indian Journal of Surgical Oncology | Issue 4/2019

Abstract

Retroperitoneal liposarcoma is usually asymptomatic until it is large enough to compress the surrounding organs. Here, we report a rare atypical case of primary retroperitoneal dedifferentiated liposarcoma who presented primarily with the misguiding and challenging paraneoplastic symptoms of high-grade fever and thrombocytosis instead of demonstrating the usual compressive symptoms. Such an extremely rare clinical presentation may mislead the diagnostic and treatment approach towards the search for medical causes, without a hint, that the tumor itself is causing these symptoms. Complete tumor excision usually leads to resolution of these paraneoplastic symptoms.

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Title: Paraneoplastic Syndrome Associated with the Retroperitoneal Dedifferentiated Liposarcoma: an Atypical Presentation and Review of the Literature
Authors: Jeewan Ram Vishnoi
Ankit Jain
Sanjeev Misra
Puneet Pareek
Meenakshi Rao
Binit Sureka
Ashok Puranik
Publication date: 01-12-2019
Publisher: Springer India
Keywords: Liposarcoma
Soft Tissue Sarcoma
Paraneoplastic Syndromes
Published in: Indian Journal of Surgical Oncology / Issue 4/2019
Print ISSN: 0975-7651
Electronic ISSN: 0976-6952
DOI: https://doi.org/10.1007/s13193-019-00971-0

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Paraneoplastic Syndrome Associated with the Retroperitoneal Dedifferentiated Liposarcoma: an Atypical Presentation and Review of the Literature

Abstract

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Abstract

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