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Published in: Italian Journal of Pediatrics 1/2014

Open Access 01-12-2014 | Case report

Congenital skin aplasia on the lower limb in a premature infant with ELBW - case report

Authors: Agata Pająk, Anna Szczygieł, Dorota Paluszyńska, Barbara Królak-Olejnik

Published in: Italian Journal of Pediatrics | Issue 1/2014

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Abstract

Aplasia cutis congenita (ACC) is usually located on the hairy scalp, on the vertex of the head, but can also occur in other locations, such as limbs, trunk. Congenital skin aplasia on the lower limb is very rare disorder. The exact etiopathogenesis is not known, but intrauterine conditions play a role in its development. ACC visually resembles an ulceration, with a smooth pink surface, which in most cases heals spontaneously. Depending on the wound size and whether signs of inflammation are present, the lesion may require local treatment. In the described case, surgical treatment was carried out because of the extreme prematurity of the infant. The outcome was satisfactory, causing no adverse impact on the child's development during the infancy.
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Metadata
Title
Congenital skin aplasia on the lower limb in a premature infant with ELBW - case report
Authors
Agata Pająk
Anna Szczygieł
Dorota Paluszyńska
Barbara Królak-Olejnik
Publication date
01-12-2014
Publisher
BioMed Central
Published in
Italian Journal of Pediatrics / Issue 1/2014
Electronic ISSN: 1824-7288
DOI
https://doi.org/10.1186/s13052-014-0088-0

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