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BMC Pulmonary Medicine
Published in: BMC Pulmonary Medicine 1/2016

Open Access 01-12-2016 | Case report

Pulmonary arterial hypertension in adult onset Still’s disease: a case report of a severe complication

Authors: L. Guilleminault, S. Laurent, A. Foucher, P. Poubeau, F. Paganin

Published in: BMC Pulmonary Medicine | Issue 1/2016

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Abstract

Background

Adult onset of Still’s disease (AOSD) is a rare systemic inflammatory disease. Cardiorespiratory complications are mainly represented by pleural and pericardial disorders and are less frequent than cutaneous and articular complaints. Pulmonary arterial hypertension (PAH) occurring in AOSD is rarely described in literature.

Case presentation

We present the case of a young patient who developed severe PAH 2 years after diagnosis of AOSD. This is a rare and severe complication which is probably underestimated.

Conclusions

PAH in AOSD can be lethal, and unfortunately its occurrence is unpredictable. Echocardiographic screening of AOSD patients should be evaluated in further trials. Currently, the most suitable treatment is still unknown.
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Metadata
Title
Pulmonary arterial hypertension in adult onset Still’s disease: a case report of a severe complication
Authors
L. Guilleminault
S. Laurent
A. Foucher
P. Poubeau
F. Paganin
Publication date
01-12-2016
Publisher
BioMed Central
Published in
BMC Pulmonary Medicine / Issue 1/2016
Electronic ISSN: 1471-2466
DOI
https://doi.org/10.1186/s12890-016-0237-x

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WHO estimates that half of all patients worldwide are non-adherent to their prescribed medication. The consequences of poor adherence can be catastrophic, on both the individual and population level.

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