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Published in: The Journal of Headache and Pain 1/2018

Open Access 01-12-2018 | Consensus article

European Headache Federation guideline on idiopathic intracranial hypertension

Authors: Jan Hoffmann, Susan P Mollan, Koen Paemeleire, Christian Lampl, Rigmor H Jensen, Alexandra J Sinclair

Published in: The Journal of Headache and Pain | Issue 1/2018

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Abstract

Background

Idiopathic Intracranial Hypertension (IIH) is characterized by an elevation of intracranial pressure (ICP no identifiable cause. The aetiology remains largely unknown, however observations made in a number of recent clinical studies are increasing the understanding of the disease and now provide the basis for evidence-based treatment strategies.

Methods

The Embase, CDSR, CENTRAL, DARE and MEDLINE databases were searched up to 1st June 2018. We analyzed randomized controlled trials and systematic reviews that investigate IIH.

Results

Diagnostic uncertainty, headache morbidity and visual loss are among the highest concerns of clinicians and patients in this disease area. Research in this field is infrequent due to the rarity of the disease and the lack of understanding of the underlying pathology.

Conclusions

This European Headache Federation consensus paper provides evidence-based recommendations and practical advice on the investigation and management of IIH.
Appendix
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Metadata
Title
European Headache Federation guideline on idiopathic intracranial hypertension
Authors
Jan Hoffmann
Susan P Mollan
Koen Paemeleire
Christian Lampl
Rigmor H Jensen
Alexandra J Sinclair
Publication date
01-12-2018
Publisher
Springer Milan
Published in
The Journal of Headache and Pain / Issue 1/2018
Print ISSN: 1129-2369
Electronic ISSN: 1129-2377
DOI
https://doi.org/10.1186/s10194-018-0919-2

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