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Open Access 01-12-2014 | Case report

Primary desmoplastic small round cell tumor of the duodenum

Authors: Qi Liu, Nan Liu, DeXing Chen

Published in: European Journal of Medical Research | Issue 1/2014

Abstract

The desmoplastic small round cell tumor (DSRCT) is an extremely rare tumor that mainly affects adolescents and mostly involves the abdominal and pelvic peritoneum. A 14-year-old girl presented with intermittent epigastric pain; abdominal computed tomography and upper gastrointestinal barium X-ray revealed an 8 cm × 10 cm space-occupying mass in the duodenal region. The patient underwent pancreaticoduodenectomy and the final pathologic diagnosis was DSRCT. Although multi-agent systemic chemotherapy was given, the patient died of metastasis 8 months later. Early diagnosis and surgical treatment with adjuvant chemotherapy seems to be the best treatment choice for this disease.

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Title: Primary desmoplastic small round cell tumor of the duodenum
Authors: Qi Liu
Nan Liu
DeXing Chen
Publication date: 01-12-2014
Publisher: BioMed Central
Published in: European Journal of Medical Research / Issue 1/2014
Electronic ISSN: 2047-783X
DOI: https://doi.org/10.1186/2047-783X-19-38

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Primary desmoplastic small round cell tumor of the duodenum

Abstract

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