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Open Access 01-12-2014 | Case report
Bone metastases from bladder perivascular epithelioid cell tumor – an unusual localization of a rare tumor: a case report
Published in: Journal of Medical Case Reports | Issue 1/2014
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Introduction
Perivascular epithelioid cell tumors are mesenchymal tumors composed of histologically and immunohistochemically distinctive perivascular epithelioid cells. This type of tumor is rare but bladder localization is even rarer.
Case presentation
A case of bone metastatic bladder perivascular epithelioid cell tumor in a 65-year-old Caucasian man treated with surgery and chemotherapy is described and compared with other reports in the literature.
Conclusions
The rarity of perivascular epithelioid cell tumors hinders the development of a standard therapeutic approach, and thus requires case report descriptions. There is a need for cooperative studies to enlarge the case series and establish the best treatment strategy for this rare disease.