Top

Published in:

Open Access 01-12-2011 | Case report

Superior canal dehiscence in a patient with three failed stapedectomy operations for otosclerosis: a case report

Published in: Journal of Medical Case Reports | Issue 1/2011

Abstract

Introduction

This case illustrates that superior semicircular canal dehiscence syndrome can be associated with a "pseudo"-conductive hearing loss, a symptom that overlaps with the clinical appearance of otosclerosis.

Case presentation

We present the case of a 48-year-old German Caucasian woman presenting with hearing loss on the left side and vertigo. She had undergone three previous stapedectomies for hearing improvement. Reformatted high-resolution computed tomographic scanning and the patient's history confirmed the diagnosis of concurrent canal dehiscence syndrome.

Conclusion

Failure of hearing improvement after otosclerosis surgery may indicate an alternative underlying diagnosis which should be explored by further appropriate evaluation.

Available only for authorised users

Ramsey MJ, McKenna MJ, Barker FG: Superior semicircular canal dehiscence syndrome: case report. J Neurosurg. 2004, 100: 123-124. 10.3171/jns.2004.100.1.0123.CrossRefPubMed

Minor LB: Superior canal dehiscence syndrome. Am J Otol. 2000, 21: 9-19.CrossRefPubMed

Hope A, Fagan P: Latent superior canal dehiscence syndrome unmasked by stapedotomy for otosclerosis. J Laryngol Otol. 2010, 124: 428-430. 10.1017/S0022215109991654.CrossRefPubMed

Zhou G, Gopen Q, Poe DS: Clinical and diagnostic characterization of canal dehiscence syndrome: a great otologic mimicker. Otol Neurotol. 2007, 28: 920-926. 10.1097/MAO.0b013e31814b25f2.CrossRef

Banerjee A, Whyte A, Atlas MD: Superior canal dehiscence: review of a new condition. Clin Otolaryngol. 2005, 30: 9-15. 10.1111/j.1365-2273.2004.00940.x.CrossRefPubMed

Mikulec AA, McKenna MJ, Ramsey MJ, Rosowski JJ, Herrmann BS, Rauch SD, Curtin HD, Merchant SN: Superior semicircular canal dehiscence presenting as conductive hearing loss without vertigo. Otol Neurotol. 2004, 25: 121-129. 10.1097/00129492-200403000-00007.CrossRefPubMed

Modugno G, Brandolini C, Savastio G, Ceroni AR, Pirodda A: Superior semicircular canal dehiscence: a series of 13 cases. ORL J Otorhinolaryngol Relat Spec. 2005, 67: 180-184.CrossRefPubMed

Hillman TA, Kertesz TR, Hadley K, Shelton C: Reversible peripheral vestibulopathy: the treatment of superior canal dehiscence. Otolaryngol Head Neck Surg. 2006, 134: 431-436. 10.1016/j.otohns.2005.10.033.CrossRefPubMed

Schmuziger N, Allum J, Buitrago-Téllez C, Probst R: Incapacitating hypersensitivity to one's own body sounds due to a dehiscence of bone overlying the superior semicircular canal: a case report. Eur Arch Otorhinolaryngol. 2006, 263: 69-74. 10.1007/s00405-005-0939-9.CrossRefPubMed

10.

Limb CJ, Carey JP, Srireddy S, Minor LB: Auditory function in patients with surgically treated superior semicircular canal dehiscence. Otol Neurotol. 2006, 27: 969-980. 10.1097/01.mao.0000235376.70492.8e.CrossRefPubMed

11.

Rosowski JJ, Songer JE, Nakajima HH, Brinsko KM, Merchant SN: Clinical, experimental, and theoretical investigations of the effect of superior semicircular canal dehiscence on hearing mechanisms. Otol Neurotol. 2004, 25: 323-332. 10.1097/00129492-200405000-00021.CrossRefPubMed

12.

Songer JE, Rosowski JJ: The effect of superior canal dehiscence on cochlear potential in response to air-conducted stimuli in chinchilla. Hear Res. 2005, 210: 53-62. 10.1016/j.heares.2005.07.003.CrossRefPubMedPubMedCentral

13.

Songer JE, Rosowski JJ: The effect of superior-canal opening on middle-ear input admittance and air-conducted stapes velocity in chinchilla. J Acoust Soc Am. 2006, 120: 258-269. 10.1121/1.2204356.CrossRefPubMedPubMedCentral

14.

Minor LB, Carey JP, Cremer PD, Lustig LR, Streubel SO, Ruckenstein MJ: Dehiscence of bone overlying the superior canal as a cause of apparent conductive hearing loss. Otol Neurotol. 2003, 24: 270-278. 10.1097/00129492-200303000-00023.CrossRefPubMed

15.

Chien W, Ravicz ME, Rosowski JJ, Merchant SN: Measurements of human middle- and inner-ear mechanics with dehiscence of the superior semicircular canal. Otol Neurotol. 2007, 28: 250-257. 10.1097/01.mao.0000244370.47320.9a.CrossRefPubMedPubMedCentral

16.

Songer JE, Rosowski JJ: A mechano-acoustic model of the effect of superior canal dehiscence on hearing in chinchilla. J Acoust Soc Am. 2007, 122: 943-951. 10.1121/1.2747158.CrossRefPubMedPubMedCentral

17.

Silverstein H, Van Ess MJ: Complete round window niche occlusion for superior semicircular canal dehiscence syndrome: a minimally invasive approach. Ear Nose Throat J. 2009, 88: 1042-1056.PubMed

18.

Mikulec AA, Poe DS, McKenna MJ: Operative management of superior semicircular canal dehiscence. Laryngoscope. 2005, 115: 501-507. 10.1097/01.mlg.0000157844.48036.e7.CrossRefPubMed

Title: Superior canal dehiscence in a patient with three failed stapedectomy operations for otosclerosis: a case report
Publication date: 01-12-2011
Published in: Journal of Medical Case Reports / Issue 1/2011
Electronic ISSN: 1752-1947
DOI: https://doi.org/10.1186/1752-1947-5-47

Keynote webinar | Spotlight on sleep in brain health

Springer Medicine

Superior canal dehiscence in a patient with three failed stapedectomy operations for otosclerosis: a case report

Abstract

Introduction

Case presentation

Conclusion

Keynote webinar | Spotlight on sleep in brain health

Springer Medicine

Abstract

Introduction

Case presentation

Conclusion

Please log in to get access to this content

Other articles of this Issue 1/2011

Complications of nephrogenic systemic fibrosis following repeated exposure to gadolinium in a man with hypothyroidism: a case report

Steinert's syndrome presenting as anal incontinence: a case report

Itraconazole associated quadriparesis and edema: a case report

Vaughan-Jackson-like syndrome as an unusual presentation of Kienböck's disease: a case report

Laparoscopic resection of a lymphangiomatous cyst of the colon: a case report

Subacute dislocation of the elbow following Galeazzi fracture-dislocation of the radius: A case report