Skip to main content
Top
Published in: Journal of Medical Case Reports 1/2010

Open Access 01-12-2010 | Case report

Dentin dysplasia type I: a case report and review of the literature

Authors: Lida Toomarian, Fatemeh Mashhadiabbas, Mahkameh Mirkarimi, Leili Mehrdad

Published in: Journal of Medical Case Reports | Issue 1/2010

Login to get access

Abstract

Introduction

Dentin dysplasia is a rare hereditary disturbance of dentin formation characterized by defective dentin development with clinically normal appearing crowns, severe hypermobility of teeth and spontaneous dental abscesses or cysts. Radiographic analysis shows obliteration of all pulp chambers, short, blunted and malformed or absent roots and peri-apical radiolucencies of non carious teeth.

Case presentation

We present a case of dentin dysplasia type I in a 12-year-old Iranian boy, and the clinical, radiographic and histopathologic findings of this condition and treatment are described.

Conclusions

There are still many inconclusive issues in the diagnosis and management of patients with dentin dysplasia. The diagnostic features of this rare disturbance will remain incompletely defined until additional cases have been described. Early diagnosis of the condition and initiation of effective regular dental treatments may help these patients to prevent or delay loss of dentition.
Appendix
Available only for authorised users
Literature
1.
go back to reference Kim JW, Simmer JP: Hereditary dentin defects. Dent Res. 2007, 86: 392-399. 10.1177/154405910708600502.CrossRef Kim JW, Simmer JP: Hereditary dentin defects. Dent Res. 2007, 86: 392-399. 10.1177/154405910708600502.CrossRef
2.
go back to reference Ballschmiede G: Dissertation, Berlin, 1920. Malformations of the Jaws and Teeth. Edited by: Herbst E, Apffelstaedt M. 1930, New York: Oxford University Press, 286- Ballschmiede G: Dissertation, Berlin, 1920. Malformations of the Jaws and Teeth. Edited by: Herbst E, Apffelstaedt M. 1930, New York: Oxford University Press, 286-
3.
go back to reference Rushton MA: A case of dentinal dysplasia. Guy's Hospital Report. 1939, 89: 369-373. Rushton MA: A case of dentinal dysplasia. Guy's Hospital Report. 1939, 89: 369-373.
4.
go back to reference Witkop CJ Jr: Hereditary defects of dentin. Dent Clin North Am. 1975, 19: 25-45.PubMed Witkop CJ Jr: Hereditary defects of dentin. Dent Clin North Am. 1975, 19: 25-45.PubMed
5.
go back to reference Neville B, Damm D, Allen C, Bouquot J: Oral and Maxillofacial Pathology. 2008, Elsevier, 3 Neville B, Damm D, Allen C, Bouquot J: Oral and Maxillofacial Pathology. 2008, Elsevier, 3
6.
go back to reference Regezi JA, Sciubba JJ, Jordan RCK: Oral Pathology Clinical Pathologic Correlations. 2008, Saunders, 5 Regezi JA, Sciubba JJ, Jordan RCK: Oral Pathology Clinical Pathologic Correlations. 2008, Saunders, 5
7.
go back to reference Logan J, Becks H, Silverman S, Pinborg JJ: Dentinal dysplasia. Oral Surg. 1962, 15: 317-333. 10.1016/0030-4220(62)90113-5.CrossRefPubMed Logan J, Becks H, Silverman S, Pinborg JJ: Dentinal dysplasia. Oral Surg. 1962, 15: 317-333. 10.1016/0030-4220(62)90113-5.CrossRefPubMed
8.
go back to reference Wesley RK, Wysocki GP, Mintz SM, Jackson J: Dentin dysplasia type I. Oral Surg. 1976, 41: 516-524. 10.1016/0030-4220(76)90279-6.CrossRefPubMed Wesley RK, Wysocki GP, Mintz SM, Jackson J: Dentin dysplasia type I. Oral Surg. 1976, 41: 516-524. 10.1016/0030-4220(76)90279-6.CrossRefPubMed
9.
go back to reference Perl T, Farman AG, Elizabeth P, Town C: Radicular (Type I) dentin dysplasia. Oral Surg Oral Med Oral Pathol. 1977, 43: 746-753. 10.1016/0030-4220(77)90060-3.CrossRefPubMed Perl T, Farman AG, Elizabeth P, Town C: Radicular (Type I) dentin dysplasia. Oral Surg Oral Med Oral Pathol. 1977, 43: 746-753. 10.1016/0030-4220(77)90060-3.CrossRefPubMed
10.
go back to reference Morris ME, Augsburger RH: Dentine dysplasia with sclerotic bone and skeletal anomalies inherited as an autosomal dominant trait. Oral Surg Oral Med Oral Pathol. 1977, 43: 267-283. 10.1016/0030-4220(77)90163-3.CrossRefPubMed Morris ME, Augsburger RH: Dentine dysplasia with sclerotic bone and skeletal anomalies inherited as an autosomal dominant trait. Oral Surg Oral Med Oral Pathol. 1977, 43: 267-283. 10.1016/0030-4220(77)90163-3.CrossRefPubMed
11.
go back to reference Elzay RP, Robinson CT: Dentinal dysplasia, report of a case. Oral Surg. 1967, 23: 338-342. 10.1016/0030-4220(67)90146-6.CrossRefPubMed Elzay RP, Robinson CT: Dentinal dysplasia, report of a case. Oral Surg. 1967, 23: 338-342. 10.1016/0030-4220(67)90146-6.CrossRefPubMed
12.
go back to reference Ozer L, Karasu H, Aras K, Tokman B, Ersoy E: Dentin dysplasia type I: report of atypical cases in the permanent and mixed dentitions. Med Oral Pathol Oral Radiol Endod. 2004, 98: 85-90. 10.1016/j.tripleo.2004.01.005.CrossRef Ozer L, Karasu H, Aras K, Tokman B, Ersoy E: Dentin dysplasia type I: report of atypical cases in the permanent and mixed dentitions. Med Oral Pathol Oral Radiol Endod. 2004, 98: 85-90. 10.1016/j.tripleo.2004.01.005.CrossRef
13.
go back to reference Ravanshad SH, Khayat A: Endodontic therapy on a dentition exhibiting multiple periapical radiolucencies associated with dentinal dysplasia type 1. Aust Endod J. 2006, 32: 40-42. 10.1111/j.1747-4477.2006.00008.x.CrossRefPubMed Ravanshad SH, Khayat A: Endodontic therapy on a dentition exhibiting multiple periapical radiolucencies associated with dentinal dysplasia type 1. Aust Endod J. 2006, 32: 40-42. 10.1111/j.1747-4477.2006.00008.x.CrossRefPubMed
14.
go back to reference Ansari G, Reid JS: Dentinal dysplasia type I: review of the literature and report of a family. ASDC J Dent Child. 1997, 64: 429-434.PubMed Ansari G, Reid JS: Dentinal dysplasia type I: review of the literature and report of a family. ASDC J Dent Child. 1997, 64: 429-434.PubMed
15.
go back to reference Muñoz-Guerra MF, Naval-Gías L, Escorial V, Sastre-Pérez J: Dentin dysplasia type I treated with onlay bone grafting, sinus augmentation, and osseointegrated implants. Implant Dent. 2006, 15: 248-253. 10.1097/01.id.0000234638.60877.1b.CrossRefPubMed Muñoz-Guerra MF, Naval-Gías L, Escorial V, Sastre-Pérez J: Dentin dysplasia type I treated with onlay bone grafting, sinus augmentation, and osseointegrated implants. Implant Dent. 2006, 15: 248-253. 10.1097/01.id.0000234638.60877.1b.CrossRefPubMed
Metadata
Title
Dentin dysplasia type I: a case report and review of the literature
Authors
Lida Toomarian
Fatemeh Mashhadiabbas
Mahkameh Mirkarimi
Leili Mehrdad
Publication date
01-12-2010
Publisher
BioMed Central
Published in
Journal of Medical Case Reports / Issue 1/2010
Electronic ISSN: 1752-1947
DOI
https://doi.org/10.1186/1752-1947-4-1

Other articles of this Issue 1/2010

Journal of Medical Case Reports 1/2010 Go to the issue