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Published in: World Journal of Surgical Oncology 1/2006

Open Access 01-12-2006 | Case report

Clear cell sarcoma of the scapula. A case report and review of the literature

Authors: Constantinos J Kazakos, Vasilios G Galanis, Alexandra Giatromanolaki, Dennis-Alexander J Verettas, Efthimios Sivridis

Published in: World Journal of Surgical Oncology | Issue 1/2006

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Abstract

Background

Clear cell sarcoma of tendons and aponeuroses (CCSTA) appears usually in the extremities and rarely in the trunk.

Case presentation

We present an unusual case of CCSTA overlying the scapular region and with secondary osseous extension in the lower scapula. The patient underwent a wide local excision with removal of the tumor and the lower two thirds of the scapula. He had no local recurrences but he developed lung metastases after 5 months in spite of postoperative chemotherapy. He finally died ten months later.

Conclusion

The patients with CCSTA have a variable unpredictable course. Despite treatment the overall prognosis is poor.
Appendix
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Metadata
Title
Clear cell sarcoma of the scapula. A case report and review of the literature
Authors
Constantinos J Kazakos
Vasilios G Galanis
Alexandra Giatromanolaki
Dennis-Alexander J Verettas
Efthimios Sivridis
Publication date
01-12-2006
Publisher
BioMed Central
Published in
World Journal of Surgical Oncology / Issue 1/2006
Electronic ISSN: 1477-7819
DOI
https://doi.org/10.1186/1477-7819-4-48

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