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World Journal of Surgical Oncology

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Open Access 01-12-2004 | Case report

Small bowel gastrointestinal stromal tumours and ampullary cancer in Type 1 neurofibromatosis

Authors: Kasim A Behranwala, Duncan Spalding, Andrew Wotherspoon, Cyril Fisher, Jeremy N Thompson

Published in: World Journal of Surgical Oncology | Issue 1/2004

Abstract

Background

Type 1 neurofibromatosis (NF-1) is an autosomal dominant disorder with variable penetrance; approximately 50% of cases present as new mutations

Case report

We report a case of a 56 year-old man with Von Recklinghausen's disease, carcinoma of the ampulla of Vater and incidental benign gastrointestinal stromal tumours of the jejunum.

Conclusions

Coexistence between ampullary carcinoid, ectopic pancreatic tissue in the jejunum and neurofibroma of the jejunum in NF-1 has been previously described however; the association of synchronous carcinoma of the ampulla of Vater and gastrointestinal stromal tumour of the jejunum in NF-1 has not been previously reported.

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Title: Small bowel gastrointestinal stromal tumours and ampullary cancer in Type 1 neurofibromatosis
Authors: Kasim A Behranwala
Duncan Spalding
Andrew Wotherspoon
Cyril Fisher
Jeremy N Thompson
Publication date: 01-12-2004
Publisher: BioMed Central
Published in: World Journal of Surgical Oncology / Issue 1/2004
Electronic ISSN: 1477-7819
DOI: https://doi.org/10.1186/1477-7819-2-1

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Small bowel gastrointestinal stromal tumours and ampullary cancer in Type 1 neurofibromatosis

Abstract

Background

Case report

Conclusions

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Abstract

Background

Case report

Conclusions

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