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Open Access 01-12-2014 | Case report

Primitive neuroectodermal tumor (PNET) of the lung in an adult woman

Authors: Mariam Gachechiladze, Josef Škarda, Maha Ibrahim, Tomáš Tichý, Patrik Flodr, Pavla Latálová, Jiří Ehrmann, Radek Trojanec, Zdenek Kolář

Published in: World Journal of Surgical Oncology | Issue 1/2014

Abstract

Primary primitive neuroectodermal tumors (PNETs) are extremely rare in the lung and especially in adult women. We describe a case of PNET of the lung with aggressive behavior in 31-year-old woman. Diagnosis was based on histopathological and immunohistochemical studies, and confirmed by molecular genetic analysis of chromosome rearrangements in the EWSR1 gene region. Clinical follow-up, post-mortem findings, and differential diagnosis are also discussed.

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Title: Primitive neuroectodermal tumor (PNET) of the lung in an adult woman
Authors: Mariam Gachechiladze
Josef Škarda
Maha Ibrahim
Tomáš Tichý
Patrik Flodr
Pavla Latálová
Jiří Ehrmann
Radek Trojanec
Zdenek Kolář
Publication date: 01-12-2014
Publisher: BioMed Central
Published in: World Journal of Surgical Oncology / Issue 1/2014
Electronic ISSN: 1477-7819
DOI: https://doi.org/10.1186/1477-7819-12-374

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Primitive neuroectodermal tumor (PNET) of the lung in an adult woman

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