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Published in: Cardiovascular Ultrasound 1/2005

Open Access 01-12-2005 | Case report

Mitral supravalvular ring: a case report

Authors: Walter Serra, Paola Testa, Diego Ardissino

Published in: Cardiovascular Ultrasound | Issue 1/2005

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Abstract

Supravalvular mitral stenosis is a rare condition characterized by an abnormal ridge, with one or two orifices, covering and obstructing the mitral valve. Preoperative diagnosis is difficult with transtoracic echo (TTE), angiography and magnetic resonance imaging (MRI).
In this case, a 36-year-old male, was admitted to our Heart department: He experienced progressive dyspnea on effort and at rest.
Diagnosis was made by transesophageal echocardiography which showed, on apical 4-chamber section, an anulare structure attached since a membrane to the atrial wall anterior mitral valve leaflet and just proximal to the posterior mitral leaflet.
Pre-operative identification of the supravalvular mitral ring is the target for obtaining good surgical results. Cineangiography and MRI both failed in reaching this objective, whereas, transesophageal echocardiography is the best method to identify this congenital heart disease.
Using TEE the identification is not only possible but also easier.
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Metadata
Title
Mitral supravalvular ring: a case report
Authors
Walter Serra
Paola Testa
Diego Ardissino
Publication date
01-12-2005
Publisher
BioMed Central
Published in
Cardiovascular Ultrasound / Issue 1/2005
Electronic ISSN: 1476-7120
DOI
https://doi.org/10.1186/1476-7120-3-19

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