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Published in: BMC Pediatrics 1/2022

Open Access 01-12-2022 | Lipoma | Case report

Concomitant spinal dural arteriovenous fistula and nodular fasciitis in an adolescent: case report

Authors: Chan-Lin Chu, Yu-Jen Lu, Tsong-Hai Lee, Shih-Ming Jung, Yu-Cheng Chu, Ho-Fai Wong

Published in: BMC Pediatrics | Issue 1/2022

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Abstract

Background

Spinal dural arteriovenous fistula (SDAVF) usually occurs during the 4th to 6th decades of life, and adolescent SDAVF is rarely reported. SDAVF arising around a tumor is also rare, and reported tumors are mostly schwannoma and lipoma.

Case presentation

We reported a 16-year-old male presented with progressive weakness and numbness of lower limbs for 3 months. A SDAVF was found, which was fed by right radicular arteries from segmental artery at L2 level and drained retrogradely into perimedullary veins. A concomitant spinal extradural nodular fasciitis at right L1/L2 intervertebral foramen was also noted. The SDAVF was completely obliterated by endovascular treatment and the tumor was debulked. The patient recovered well after the procedures.

Conclusions

Our case report suggests SDAVF can occur in adolescent. The concomitant presence with a nodular fasciitis indicates that although it usually arises in subcutaneous tissue but can rarely form on the dura of spine.
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Metadata
Title
Concomitant spinal dural arteriovenous fistula and nodular fasciitis in an adolescent: case report
Authors
Chan-Lin Chu
Yu-Jen Lu
Tsong-Hai Lee
Shih-Ming Jung
Yu-Cheng Chu
Ho-Fai Wong
Publication date
01-12-2022
Publisher
BioMed Central
Published in
BMC Pediatrics / Issue 1/2022
Electronic ISSN: 1471-2431
DOI
https://doi.org/10.1186/s12887-021-03032-0

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