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Published in: World Journal of Surgical Oncology 1/2005

Open Access 01-12-2005 | Case report

Case report: late perianal mucinous adenocarcinoma after Crohn's disease proctectomy: an oncological rarity

Authors: Michael Keese, Walter Back, Dietmar Dinter, Rainer Gladisch, Andreas Joos, Pablo Palma

Published in: World Journal of Surgical Oncology | Issue 1/2005

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Abstract

Background

As in ulcerative colitis, there is an increased incidence of colorectal carcinoma in Crohn's disease. While carcinoma formation originating from ano-rectal fistulas is generally considered as a rare event there are different publications reporting on mucinous adenocarcinoma formation in association with a neovagina and rectovaginal fistulas. To the best of our knowledge this is the first description of a perianal mucinous adenocarcinoma arising in a patient after Crohn's disease proctocolectomy.

Case presentation

We report the case of a 50-year old female with a mucinous adenocarcinoma forming in the perineum eleven years after proctocolectomy for Crohn's disease. The patient was readmitted with perineal pain, leucocytosis and a perineal mass highly suspicious of abscess formation in the MRI-Scan. Histological examination revealed a mucinous adenocarcinoma. Exenteration including vagina, uterus and ovaries together with the coccygeal-bone was performed.

Conclusion

Mucinous adenocarcinoma formation is a rare complication of Crohn's disease and so far unreported after proctocolectomy.
Appendix
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Metadata
Title
Case report: late perianal mucinous adenocarcinoma after Crohn's disease proctectomy: an oncological rarity
Authors
Michael Keese
Walter Back
Dietmar Dinter
Rainer Gladisch
Andreas Joos
Pablo Palma
Publication date
01-12-2005
Publisher
BioMed Central
Published in
World Journal of Surgical Oncology / Issue 1/2005
Electronic ISSN: 1477-7819
DOI
https://doi.org/10.1186/1477-7819-3-42

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