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01-06-2017 | Case report

Rare Case Report of Alveolar Soft Part Sarcoma of the Orbit

Authors: G kranthi kumar, Hemant Nemade, Krishnamohan, Daphne Fonseca, L.M.Chandra Sekhara Rao, T.Subramanyeshwar Rao

Published in: Indian Journal of Surgical Oncology | Issue 2/2017

Abstract

Alveolar soft part sarcoma (ASPS) is a rare but distinct soft tissue tumor with unique histopathological and electron microscopic features. Orbital involvement is rare with only few reports published in the literature. ASPS have an indolent clinical course, but it is known to metastasize. Primary modality of treatment is surgery followed by adjuvant treatment. This case is a unique presentation with orbital mass with on and off bleeding. This is the largest orbital ASPS for which orbital exenteration was performed.

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Title: Rare Case Report of Alveolar Soft Part Sarcoma of the Orbit
Authors: G kranthi kumar
Hemant Nemade
Krishnamohan
Daphne Fonseca
L.M.Chandra Sekhara Rao
T.Subramanyeshwar Rao
Publication date: 01-06-2017
Publisher: Springer India
Published in: Indian Journal of Surgical Oncology / Issue 2/2017
Print ISSN: 0975-7651
Electronic ISSN: 0976-6952
DOI: https://doi.org/10.1007/s13193-016-0550-0

At a glance: The STEP trials

Springer Medicine

Rare Case Report of Alveolar Soft Part Sarcoma of the Orbit

Abstract

At a glance: The STEP trials

Springer Medicine

Abstract

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