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Open Access 01-12-2013 | Case Report

A calcified sinutubular junction: the discovery of a supravalvular aortic stenosis in an elderly woman

Authors: L. Cozijnsen, M. Bakker-de Boo, J. J. Kardux, B. J. Bouma

Published in: Netherlands Heart Journal | Issue 12/2013

Abstract

We report a case of a 64 year old woman with a calcified ring at the level of the sinotubular junction. Echocardiography and Computed Tomography showed a supravalvular aortic stenosis, without known associated lesions, except for the existence of an aberrant right subclavian artery. These combination of abnormalities makes it an unique case. Differential diagnosis of sinutubular calcification is added. From the literature a short review of supravalvular aortic stenosis is presented with indications for surgical intervention. Lifelong and regular follow up is necessary.

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Title: A calcified sinutubular junction: the discovery of a supravalvular aortic stenosis in an elderly woman
Authors: L. Cozijnsen
M. Bakker-de Boo
J. J. Kardux
B. J. Bouma
Publication date: 01-12-2013
Publisher: Bohn Stafleu van Loghum
Published in: Netherlands Heart Journal / Issue 12/2013
Print ISSN: 1568-5888
Electronic ISSN: 1876-6250
DOI: https://doi.org/10.1007/s12471-013-0426-7

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