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Indian Journal of Thoracic and Cardiovascular Surgery

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01-07-2018 | Case report

Left parasternal approach for Bentall procedure in a patient of Marfan syndrome with severe pectus excavatum

Authors: Pankaj Aggarwal, Sachin Mahajan, Siddharth Garg

Published in: Indian Journal of Thoracic and Cardiovascular Surgery | Issue 3/2018

Abstract

Annuloaortic ectasia with ascending aortic aneurysm with severe aortic regurgitation with severe left ventricular dysfunction is a serious condition especially in patients with Marfan syndrome (MFS) simultaneously having severe pectus excavatum (PE) deformity. We report our left parasternal approach in such patient in whom median sternotomy was not feasible. We achieved excellent exposure of dislocated heart and great vessels enabling Bentall procedure. Since patient did not consent for combined correction of chest wall deformity, we plan to undertake it later. Therefore, we conclude that left parasternal approach is feasible for standard aortic root replacement surgery in severe PE.

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Title: Left parasternal approach for Bentall procedure in a patient of Marfan syndrome with severe pectus excavatum
Authors: Pankaj Aggarwal
Sachin Mahajan
Siddharth Garg
Publication date: 01-07-2018
Publisher: Springer Singapore
Published in: Indian Journal of Thoracic and Cardiovascular Surgery / Issue 3/2018
Print ISSN: 0970-9134
Electronic ISSN: 0973-7723
DOI: https://doi.org/10.1007/s12055-017-0611-1

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Left parasternal approach for Bentall procedure in a patient of Marfan syndrome with severe pectus excavatum

Abstract

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Abstract

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