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Published in: Indian Journal of Thoracic and Cardiovascular Surgery 1/2018

01-01-2018 | Case report

Pleuropulmonary blastoma—a case report and review of literature

Authors: Suraj Wasudeo Nagre, Krishnarao Narayanrao Bhosle, Asif Shaikh, Vignesh Ravikumar

Published in: Indian Journal of Thoracic and Cardiovascular Surgery | Special Issue 1/2018

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Abstract

Pleuropulmonary blastoma (PPB) is a very rare, highly aggressive and malignant tumour originating from either the lungs or pleura. It occurs mainly in children of less than 5 or 6 years but may occur in adults rarely. It has a poor prognosis with three different subtypes: cystic (type I), combined cystic and solid (type II) and solid (type III). The PPB should be treated aggressively with surgery and chemotherapy. Here, we report a case of a 14-year-old boy presenting with acute respiratory distress because of left-side PPB. He underwent left-side thoracotomy with surgical resection of PPB followed by adjuvant chemotherapy.
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Metadata
Title
Pleuropulmonary blastoma—a case report and review of literature
Authors
Suraj Wasudeo Nagre
Krishnarao Narayanrao Bhosle
Asif Shaikh
Vignesh Ravikumar
Publication date
01-01-2018
Publisher
Springer Singapore
Published in
Indian Journal of Thoracic and Cardiovascular Surgery / Issue Special Issue 1/2018
Print ISSN: 0970-9134
Electronic ISSN: 0973-7723
DOI
https://doi.org/10.1007/s12055-017-0574-2

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