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Published in: Immunologic Research 2/2017

01-04-2017 | Novel Aspects in Lupus, 2017

Thrombotic thrombocytopenic purpura in a new onset lupus patient?

Authors: Nery Sablón González, Noel Lorenzo, Yanet Parodis, Maria Belen Alonso Ortiz, Melek Kechida, Jose Carlos Rodriguez Perez

Published in: Immunologic Research | Issue 2/2017

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Abstract

We are presenting a case of TTP with undetectable levels of ADAMTS 13 in a 39-year-old woman. Diagnosis of systemic lupus was evoked in the setting of thrombotic microangiopathy. The patient presented normal renal function but important neurological impairment. Treatment with daily plasmapheresis as well as Rituximab, cyclophosphamide as steroids was required to achieve clinical improvement.
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Metadata
Title
Thrombotic thrombocytopenic purpura in a new onset lupus patient?
Authors
Nery Sablón González
Noel Lorenzo
Yanet Parodis
Maria Belen Alonso Ortiz
Melek Kechida
Jose Carlos Rodriguez Perez
Publication date
01-04-2017
Publisher
Springer US
Published in
Immunologic Research / Issue 2/2017
Print ISSN: 0257-277X
Electronic ISSN: 1559-0755
DOI
https://doi.org/10.1007/s12026-017-8898-y

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