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Current Rheumatology Reports
Published in: Current Rheumatology Reports 11/2017

01-11-2017 | Imaging (D Mintz, Section Editor)

Cardiopulmonary Manifestations of Collagen Vascular Diseases

Authors: Hamza Jawad, Sebastian R. McWilliams, Sanjeev Bhalla

Published in: Current Rheumatology Reports | Issue 11/2017

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Abstract

Purpose of Review

The study aimed to illustrate the cardiopulmonary findings of the following collagen vascular diseases on cross-sectional imaging: rheumatoid arthritis, scleroderma (progressive systemic sclerosis), systemic lupus erythematosus, the inflammatory myopathies (polymyositis/dermatomyositis), and Sjögren’s syndrome.

Recent Findings

Although collagen vascular diseases can affect any part of the body, interstitial lung disease and pulmonary hypertension are the two most important cardiopulmonary complications and are responsible for the majority of morbidity and mortality in this patient population. Interstitial pneumonia with autoimmune features (IPAF) is a newly described entity that encompasses interstitial lung disease in patients with clinical, serologic, or morphologic features suggestive of but not diagnostic of collagen vascular disease; these patients are thought to have better outcomes than idiopathic interstitial pneumonias.

Summary

Interstitial lung disease and pulmonary hypertension determine the prognosis in collagen vascular disease patients. IPAF is a new term to label patients with possible collagen vascular disease-related interstitial lung disease. Collagen vascular disease patients are at increased risk for various malignancies.
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Metadata
Title
Cardiopulmonary Manifestations of Collagen Vascular Diseases
Authors
Hamza Jawad
Sebastian R. McWilliams
Sanjeev Bhalla
Publication date
01-11-2017
Publisher
Springer US
Published in
Current Rheumatology Reports / Issue 11/2017
Print ISSN: 1523-3774
Electronic ISSN: 1534-6307
DOI
https://doi.org/10.1007/s11926-017-0697-x

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