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Published in: Irish Journal of Medical Science (1971 -) 2/2019

01-05-2019 | Original Article

Long-term outcomes following partial atrioventricular septal defect (AVSD) repair in Ireland

Authors: Katie E. O’ Sullivan, Robert Fleck, Gaia Vigano, Gerard J. Fitzmaurice, Paul Cullen, Daniyal Arshad, Mohammad Abdelrahman, Alfred E. Wood, Jonathan Mc Guinness, J. Mark Redmond, Lars Nölke

Published in: Irish Journal of Medical Science (1971 -) | Issue 2/2019

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Abstract

Background

We describe the long-term results of partial atrioventricular septal defect (AVSD) repair in a single centre encompassing a 22-year period. Described are rates of survival, reoperation and complications.

Methods

We performed a retrospective review of 556 patients undergoing AVSD repair to identify the 51 patients who underwent partial AVSD repair in Our Lady’s Children’s Hospital, Crumlin, Ireland, between 1993 and 2015 with long-term follow-up where available.

Results

A total of 29 (56.8%) of patients were male and mean age at operation was 3.32 years. Mean weight was 13.2 kg. Trisomy 21 was present in 29 (56.8%). Five patients (9.6%) had undergone prior surgery. Mean cardiopulmonary bypass time was 89 ± 36 min and mean aortic cross-clamp time was 57 ± 28 min. One patient underwent partial AVSD repair and concomitant tracheal resection and extracorporeal membrane oxygenation decannulation. One patient was managed with suture atrial septal defect (ASD) closure, the remainder with patch repair of ASD and mitral cleft closure. The length of hospital stay was 9 ± 5 days. Median follow-up was 6.06 years (IQR, 1.65–10.2 years). There were no early mortalities. One patient died 1 year following surgery (1.9%). One patient required reoperation at an interval of 2 years for severe mitral regurgitation (1.9%).

Conclusions

Short- and long-term survival following partial AVSD repair in Ireland revealed excellent results compared with other published series. Reoperation incidence also compared excellently with other reports published in the literature.
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Metadata
Title
Long-term outcomes following partial atrioventricular septal defect (AVSD) repair in Ireland
Authors
Katie E. O’ Sullivan
Robert Fleck
Gaia Vigano
Gerard J. Fitzmaurice
Paul Cullen
Daniyal Arshad
Mohammad Abdelrahman
Alfred E. Wood
Jonathan Mc Guinness
J. Mark Redmond
Lars Nölke
Publication date
01-05-2019
Publisher
Springer London
Published in
Irish Journal of Medical Science (1971 -) / Issue 2/2019
Print ISSN: 0021-1265
Electronic ISSN: 1863-4362
DOI
https://doi.org/10.1007/s11845-018-1855-5

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