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Journal of Children's Orthopaedics
Published in: Journal of Children's Orthopaedics 4/2013

01-10-2013 | Original Clinical Article

Intramedullary rod fixation of fibrous dysplasia without use of bisphosphonates

Authors: Greg Gaski, Dane Hansen, Leisel M. Willis, Gary D. Bos, John R. Kean

Published in: Journal of Children's Orthopaedics | Issue 4/2013

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Abstract

Purpose

Controversy exists regarding approach to treatment of pediatric patients with fibrous dysplasia.

Methods

We retrospectively reviewed medical records of seven patients who were treated at our institution for fibrous dysplasia by intramedullary rod fixation without bisphosphonate supplementation.

Results

Seven patients with a total of ten fibrous dysplasia lesion sites surgically treated by intramedullary rod fixation were included. Of these ten lesion sites, eight demonstrated pathologic fracture at the time of fixation. Complete fracture healing was observed in all eight sites, with no incidence of recurrent pathologic fractures examined radiographically. There were no major infections or neurologic deficits, and lesions appeared to stabilize.

Conclusions

In this series, intramedullary rod fixation proved to be successful in treatment of acute pathologic fracture and incompletely healed fibrous dysplasia lesions. We observed partial resolution of fibrous dysplasia lesions at all ten sites without significant long-term complications. Following treatment, there were no refractures.

Level of evidence

Level IV, case series.
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Metadata
Title
Intramedullary rod fixation of fibrous dysplasia without use of bisphosphonates
Authors
Greg Gaski
Dane Hansen
Leisel M. Willis
Gary D. Bos
John R. Kean
Publication date
01-10-2013
Publisher
Springer Berlin Heidelberg
Published in
Journal of Children's Orthopaedics / Issue 4/2013
Print ISSN: 1863-2521
Electronic ISSN: 1863-2548
DOI
https://doi.org/10.1007/s11832-013-0522-7

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27th Annual Meeting of the Children’s Orthopaedics, Augsburg, March 1–2, 2013