Published in:
01-02-2017 | Clinical Practice: Clinical Images
Hereditary Hemorrhagic Telangiectasia (Osler–Weber–Rendu syndrome)
Published in: Journal of General Internal Medicine | Issue 2/2017
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A 79-year-old man with hereditary hemorrhagic telangiectasia (HHT, or Osler–Weber–Rendu syndrome) complicated by portal hypertension, hypoxemia from pulmonary shunting, congestive heart failure, and gastrointestinal bleeding was admitted for recurrent epistaxis. Examination revealed extensive telangiectasias on his back (Fig. 1) and classic blanching with pressure applied by a hand (Fig. 2).
Figure 1
Clinical image of the patient’s back showing multiple patches of erythema due to cutaneous telangiectasias.
Figure 2
Demonstration of the blanching over the left scapula using the examiner’s right handprint (digits 3, 4, and 5 noted by black arrows).
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