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Open Access 01-01-2018 | Original Article

International Union of Immunological Societies: 2017 Primary Immunodeficiency Diseases Committee Report on Inborn Errors of Immunity

Authors: Capucine Picard, H. Bobby Gaspar, Waleed Al-Herz, Aziz Bousfiha, Jean-Laurent Casanova, Talal Chatila, Yanick J. Crow, Charlotte Cunningham-Rundles, Amos Etzioni, Jose Luis Franco, Steven M. Holland, Christoph Klein, Tomohiro Morio, Hans D. Ochs, Eric Oksenhendler, Jennifer Puck, Mimi L. K. Tang, Stuart G. Tangye, Troy R. Torgerson, Kathleen E. Sullivan

Published in: Journal of Clinical Immunology | Issue 1/2018

Abstract

Beginning in 1970, a committee was constituted under the auspices of the World Health Organization (WHO) to catalog primary immunodeficiencies. Twenty years later, the International Union of Immunological Societies (IUIS) took the remit of this committee. The current report details the categorization and listing of 354 (as of February 2017) inborn errors of immunity. The growth and increasing complexity of the field have been impressive, encompassing an increasing variety of conditions, and the classification described here will serve as a critical reference for immunologists and researchers worldwide.

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Title: International Union of Immunological Societies: 2017 Primary Immunodeficiency Diseases Committee Report on Inborn Errors of Immunity
Authors: Capucine Picard
H. Bobby Gaspar
Waleed Al-Herz
Aziz Bousfiha
Jean-Laurent Casanova
Talal Chatila
Yanick J. Crow
Charlotte Cunningham-Rundles
Amos Etzioni
Jose Luis Franco
Steven M. Holland
Christoph Klein
Tomohiro Morio
Hans D. Ochs
Eric Oksenhendler
Jennifer Puck
Mimi L. K. Tang
Stuart G. Tangye
Troy R. Torgerson
Kathleen E. Sullivan
Publication date: 01-01-2018
Publisher: Springer US
Published in: Journal of Clinical Immunology / Issue 1/2018
Print ISSN: 0271-9142
Electronic ISSN: 1573-2592
DOI: https://doi.org/10.1007/s10875-017-0464-9

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