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The International Journal of Cardiovascular Imaging

Published in:

01-08-2019 | Review paper

Pulmonary arteriovenous malformations

Authors: Sreeshma Tellapuri, Harold S. Park, Sanjeeva P. Kalva

Published in: The International Journal of Cardiovascular Imaging | Issue 8/2019

Abstract

Pulmonary arteriovenous malformation, a condition most commonly associated with hereditary hemorrhagic telangiectasia, is an abnormal communication between the pulmonary artery and pulmonary vein without an intervening capillary communication. Although asymptomatic in ~ 50% individuals, it can present with the dreaded complications of stroke or intracranial abscess in high-risk individuals including pregnant women, if untreated. The mainstay of treatment is now endovascular embolization of the feeding artery which can alleviate the symptoms and prevent these complications. In this review, we describe the pathophysiology, methods of screening, diagnostic workup and treatment of these vascular lesions with a particular focus on the currently used embolization techniques and their outcomes.

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Title: Pulmonary arteriovenous malformations
Authors: Sreeshma Tellapuri
Harold S. Park
Sanjeeva P. Kalva
Publication date: 01-08-2019
Publisher: Springer Netherlands
Published in: The International Journal of Cardiovascular Imaging / Issue 8/2019
Print ISSN: 1569-5794
Electronic ISSN: 1875-8312
DOI: https://doi.org/10.1007/s10554-018-1479-x

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