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Clinical and Experimental Nephrology
Published in: Clinical and Experimental Nephrology 11/2020

Open Access 01-11-2020 | Glomerulonephritis | Original article

The revised version 2018 of the nationwide web-based registry system for kidney diseases in Japan: Japan Renal Biopsy Registry and Japan Kidney Disease Registry

Authors: Takaya Ozeki, Shoichi Maruyama, Michio Nagata, Akira Shimizu, Hitoshi Sugiyama, Hiroshi Sato, Hitoshi Yokoyama, the Committee for Renal Biopsy and Disease Registry of the Japanese Society of Nephrology

Published in: Clinical and Experimental Nephrology | Issue 11/2020

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Abstract

Background

The Japan Renal Biopsy Registry (J-RBR), the first nation-wide registry of renal biopsies in Japan, was established in 2007, and expanded to include non-biopsy cases as the Japan Kidney Disease Registry (J-KDR) in 2009. The J-RBR/J-KDR is one of the biggest registries for kidney diseases. It has revealed the prevalence and distribution of kidney diseases in Japan. This registry system was meant to be revised after 10 years.

Methods

In 2017, the Committees of the Japanese Society of Nephrology started a project for the revision of the J-RBR/J-KDR. The revised system was designed in such a way that the diagnoses of the patients could be selected from the Diagnosis Panel, a list covering almost all known kidney diseases, and focusing on their pathogenesis rather than morphological classification. The Diagnosis Panel consists of 22 categories (18 glomerular, 1 tubulointerstitial, 1 congenital/genetical, 1 transplant related, and 1 other) and includes 123 diagnostic names. The items for clinical diagnosis and laboratory data were also renewed, with the addition of the information on immunosuppressive treatment.

Results

The revised version of J-RBR/J-KDR came into use in January 2018. The number of cases registered under the revised system was 2748 in the first year. The total number of cases has reached to 43,813 since 2007.

Conclusion

The revised version 2018 J-RBR/J-KDR system attempts to cover all kidney diseases by focusing on their pathogenesis. It will be a new platform for the standardized registration of kidney biopsy cases that provides more systemized data of higher quality.
Appendix
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Metadata
Title
The revised version 2018 of the nationwide web-based registry system for kidney diseases in Japan: Japan Renal Biopsy Registry and Japan Kidney Disease Registry
Authors
Takaya Ozeki
Shoichi Maruyama
Michio Nagata
Akira Shimizu
Hitoshi Sugiyama
Hiroshi Sato
Hitoshi Yokoyama
the Committee for Renal Biopsy and Disease Registry of the Japanese Society of Nephrology
Publication date
01-11-2020
Publisher
Springer Singapore
Published in
Clinical and Experimental Nephrology / Issue 11/2020
Print ISSN: 1342-1751
Electronic ISSN: 1437-7799
DOI
https://doi.org/10.1007/s10157-020-01932-6

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