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19-04-2022 | Myasthenia Gravis | Letter to the Editor

Neurophysiological challenges in myasthenia gravis associated with MuSK antibodies: a case report

Authors: Gabriele Monte, Amelia Evoli, Donald B. Sanders, Anna Modoni

Published in: Neurological Sciences | Issue 7/2022

Excerpt

Repetitive nerve stimulation (RNS) in limb muscles has low sensitivity in myasthenia gravis with muscle-specific tyrosine kinase antibodies (MuSK-MG) given the predominant involvement of cranial and neck muscles [1, 2]. However, when affected muscles (i.e., facial muscles) are tested, the RNS positivity rate in MuSK-MG can be as high as 83–87% [3]. Here, we report a patient in whom electrophysiological findings challenge the accepted concept that in MG, RNS is generally abnormal in clinically weak muscles. …

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Title: Neurophysiological challenges in myasthenia gravis associated with MuSK antibodies: a case report
Authors: Gabriele Monte
Amelia Evoli
Donald B. Sanders
Anna Modoni
Publication date: 19-04-2022
Publisher: Springer International Publishing
Keyword: Myasthenia Gravis
Published in: Neurological Sciences / Issue 7/2022
Print ISSN: 1590-1874
Electronic ISSN: 1590-3478
DOI: https://doi.org/10.1007/s10072-022-06013-y

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Neurophysiological challenges in myasthenia gravis associated with MuSK antibodies: a case report

Excerpt

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