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Published in: Neurological Sciences 2/2012

01-04-2012 | Case Report

Dilated cardiomyopathy and inclusion body myositis

Authors: Piercarlo Ballo, Leandro Chiodi, Matteo Cameli, Alessandro Malandrini, Antonio Federico, Sergio Mondillo, Alfredo Zuppiroli

Published in: Neurological Sciences | Issue 2/2012

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Abstract

Inclusion body myositis (IBM) is the most common inflammatory myopathy after 50 years of age. In contrast to polymyositis and dermatomyositis, in which cardiac involvement is relatively common, current evidences indicate that IBM is not associated with cardiac disease. We report the case of a patient with biopsy-proven IBM who developed heart failure and major ventricular arrhythmias secondary to dilated cardiomyopathy few months after the clinical onset of IBM, and in whom no pathophysiologic causes explaining cardiac enlargement and dysfunction were found by laboratory and instrumental investigations. The hypothesis of a pathophysiologic association between the two conditions is discussed.
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Metadata
Title
Dilated cardiomyopathy and inclusion body myositis
Authors
Piercarlo Ballo
Leandro Chiodi
Matteo Cameli
Alessandro Malandrini
Antonio Federico
Sergio Mondillo
Alfredo Zuppiroli
Publication date
01-04-2012
Publisher
Springer Milan
Published in
Neurological Sciences / Issue 2/2012
Print ISSN: 1590-1874
Electronic ISSN: 1590-3478
DOI
https://doi.org/10.1007/s10072-011-0766-2

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