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Clinical Rheumatology
Published in: Clinical Rheumatology 3/2006

01-05-2006 | Case Report

Hypertrophic pachymeningitis and undifferentiated connective tissue disease: a case report and review of the literature

Authors: Christos E. Lampropoulos, Mollyza Zain, Wajanat Jan, Ali Nader-Sepahi, Ian H. Sabin, David P. D' Cruz

Published in: Clinical Rheumatology | Issue 3/2006

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Abstract

A 63-year-old man with hypertrophic pachymeningitis (HP) and an undifferentiated connective tissue disease is described. Combined therapy with prednisolone and azathioprine improved his symptoms. The association between an undifferentiated connective tissue disease and HP is discussed.
Literature
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Spencer WH (1879) Case of idiopathic inflammation of the spinal dura mater (pachymeningitis spinalis externa). Lancet I:836–837CrossRef
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Ranoux D, Devaux B, Lamy C, Mear JK, Roux FX, Mas JL (1992) Meningeal sarcoidosis, pseudo-meningioma and pachymeningitis of the convexity. J Neurol Neurosurg Psychiatry 55:300–303PubMedCrossRef
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Nagashima T, Maguchi S, Terayama Y et al (2000) P-ANCA-positive Wegener's granulomatosis presenting with hypertrophy pachymeningitis and multiple cranial neuropathies: case report and review of literature. Neuropathology 20:23–28CrossRefPubMed
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Li JY, Lai PH, Lam HC et al (1999) Hypertrophic cranial pachymeningitis and lymphocytic hypophysitis in Sjogren's syndrome. Neurology 52:420–423PubMed
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Yuh WT, Drew JM, Rizzo M, Ryals TJ, Sato Y, Bell WE (1990) Evaluation of pachymeningitis by contrast-enhanced MR imaging in a patient with rheumatoid disease. Am J Neuroradiol 11:1247–1248PubMed
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Kono H, Inokuma S, Nakayama H, Yamazaki J (2000) Pachymeningitis in microscopic polyangiitis (MPA): a case report and a review of central nervous system involvement in MPA. Clin Exp Rheumatol 18:397–400PubMed
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Fujimoto M, Kira J, Murai H, Yoshimura T, Takizawa K, Goto I (1993) Hypertrophic cranial pachymeningitis associated with mixed connective tissue disease; a comparison with idiopathic and infectious pachymeningitis. Int Med 32:510–512CrossRef
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Takuma H, Shimada H, Inoue Y et al (2001) Hypertrophic pachymeningitis with anti-neutrophil cytoplasmic antibody (p-ANCA) and diabetes insipidus. Acta Neurol Scand 104:397–399CrossRefPubMed
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Lam BL, Barrett DA, Glaser JS, Schatz NJ, Brown HH (1994) Visual loss from idiopathic intracranial pachymeningitis. Neurology 44:694–698PubMed
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Nishioka H, Ito H, Haraoka J, Yamada Y, Nojima H (1998) Idiopathic hypertrophic cranial pachymeningitis with accumulation of thallium-201 on single-photon emission CT. Am J Neuroradiol 19:450–453PubMed
Metadata
Title
Hypertrophic pachymeningitis and undifferentiated connective tissue disease: a case report and review of the literature
Authors
Christos E. Lampropoulos
Mollyza Zain
Wajanat Jan
Ali Nader-Sepahi
Ian H. Sabin
David P. D' Cruz
Publication date
01-05-2006
Publisher
Springer-Verlag
Published in
Clinical Rheumatology / Issue 3/2006
Print ISSN: 0770-3198
Electronic ISSN: 1434-9949
DOI
https://doi.org/10.1007/s10067-005-0018-z

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