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Pediatric and Developmental Pathology
Published in: Pediatric and Developmental Pathology 1/2004

01-02-2004 | Case Report

Fatal Congenital Systemic Juvenile Xanthogranuloma with Liver Failure

Authors: Weimin K. Hu, Anita C. Gilliam, Susan R. Wiersma, Beverly B. Dahms

Published in: Pediatric and Developmental Pathology | Issue 1/2004

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Abstract

This is the second reported patient with systemic juvenile xanthogranuloma (JXG) to die with liver failure. The infant was born with multiple skin lesions and mild hepatomegaly. Direct hyperbilirubinemia was noted on the 2nd day of life, followed by progressive hepatomegaly, cholestasis, and death at 29 days of age. At autopsy, nodular tumor infiltrates of JXG were present throughout the liver, as well as in skin, abdominal lymph nodes, spleen, and pancreas.
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Metadata
Title
Fatal Congenital Systemic Juvenile Xanthogranuloma with Liver Failure
Authors
Weimin K. Hu
Anita C. Gilliam
Susan R. Wiersma
Beverly B. Dahms
Publication date
01-02-2004
Publisher
Springer-Verlag
Published in
Pediatric and Developmental Pathology / Issue 1/2004
Print ISSN: 1093-5266
Electronic ISSN: 1615-5742
DOI
https://doi.org/10.1007/s10024-003-4040-3

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