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Published in: European Spine Journal 4/2012

Open Access 01-06-2012 | Case Report

Currarino’s triad diagnosed in an adult woman

Authors: Lotte M. E. Berghauser Pont, Clemens M. F. Dirven, Ruben Dammers

Published in: European Spine Journal | Special Issue 4/2012

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Abstract

Purpose

To report on a female patient diagnosed with Currarino’s triad in adulthood.

Case report

This case presents an adult patient with a medical history of a congenital anal atresia, a partial sacral agenesis, and a surgically treated ectopic anus. After a coincidentally observed presacral mass by MRI, due to unexplained constipation later in adulthood, Currarino’s triad was suspected in this patient. This triad consists of anorectal malformation(s), sacrococcygeal defects and a presacral mass of various origin. Further investigation confirmed the mass to be a meningocele, and showed a tethered cord and a syrinx.

Conclusions

In (young) patients with anorectal malformations, although having no other symptoms, further examination might be required to exclude Currarino’s triad. Importance of early diagnosis and multidisciplinary assessment is recommended to establish adequate treatment if needed.
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Metadata
Title
Currarino’s triad diagnosed in an adult woman
Authors
Lotte M. E. Berghauser Pont
Clemens M. F. Dirven
Ruben Dammers
Publication date
01-06-2012
Publisher
Springer-Verlag
Published in
European Spine Journal / Issue Special Issue 4/2012
Print ISSN: 0940-6719
Electronic ISSN: 1432-0932
DOI
https://doi.org/10.1007/s00586-012-2311-2

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