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01-08-2005

Klippel–Trenaunay Syndrome—Case Report and Review of the Literature

Authors: Douraid K. Shakir, M.B., Ch.B., M.R.C.P., F.I.C.M.S. (Card.), F.I.C.M.S. (Med.), Salah O.E. Arafa, M.R.C.P.

Published in: International Journal of Angiology | Issue 3/2005

Excerpt

Klippel–Trenaunay syndrome (KTS) is an autosomal-dominant disorder characterized by a triad of cutaneous vascular nevi, soft tissue or bony hypertrophy, and varicose veins or venous malformations involving one or more extremities and is often associated with chylous ascites [1]. Incidence of venous thromboembolism that has been reported to occur with this disorder is up to 22% [2,3]. We present a case of Klippel–Trenaunay syndrome with multiple pulmonary embolisms with severe venous malformation of the left lower limb. …

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Title: Klippel–Trenaunay Syndrome—Case Report and Review of the Literature
Authors: Douraid K. Shakir, M.B., Ch.B., M.R.C.P., F.I.C.M.S. (Card.), F.I.C.M.S. (Med.)
Salah O.E. Arafa, M.R.C.P.
Publication date: 01-08-2005
Publisher: Springer-Verlag
Published in: International Journal of Angiology / Issue 3/2005
Print ISSN: 1061-1711
Electronic ISSN: 1615-5939
DOI: https://doi.org/10.1007/s00547-005-2022-1

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