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Published in: Graefe's Archive for Clinical and Experimental Ophthalmology 12/2020

01-12-2020 | Cataract | Cataract

Cataract surgery in eyes with congenital ocular coloboma

Authors: Maria Phylactou, Francesco Matarazzo, Alexander Clifford Day, Badrul Hussain, Vincenzo Maurino

Published in: Graefe's Archive for Clinical and Experimental Ophthalmology | Issue 12/2020

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Abstract

Purpose

To assess the safety, efficacy, and complication rate of phacoemulsification and intraocular lens (IOL) implantation in patients with congenital uveal coloboma and to evaluate the role of pupilloplasty.

Methods

A retrospective review of 41 eyes (31 patients) with congenital coloboma that underwent phacoemulsification and IOL implantation between September 2012 and September 2018. Preoperative, intraoperative, and postoperative data were collected for analysis.

Results

The mean patient age at surgery was 53.9 years (range 15–82). The primary indication for surgery was cataract removal for visual improvement, and lens subluxation was additionally present in two eyes (5%) preoperatively. The mean preoperative corrected distance visual acuity (CDVA) was 0.90 LogMAR. Phacoemulsification surgery was performed in all cases and nine eyes (22%) had pupilloplasty for pupil reconstitution at the time of the procedure. Surgeon grade varied from trainee surgeon under supervision to consultant. Eight patients (19.5%) had posterior capsular rupture (PCR) with or without vitreous loss requiring anterior vitrectomy. Of these, 2 cases (5%) had dropped nuclear fragments requiring subsequent pars plana vitrectomy and lens fragment removal. The mean postoperative CDVA was 0.62 LogMAR (p = 0.0003).

Conclusion

Patients with iridolenticular choroidal coloboma appear to be more at risk of complications, as were cases performed by non-consultant surgeons. Contrary, patients with phakodonesis, preoperative anterior chamber vitreous, dense cataracts, and cases were iris hooks used had no significant difference at PCR rate. The risk of postoperative glare and pupilloplasty needs to be considered in cases with good visual potential to avoid a possible second procedure.
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Metadata
Title
Cataract surgery in eyes with congenital ocular coloboma
Authors
Maria Phylactou
Francesco Matarazzo
Alexander Clifford Day
Badrul Hussain
Vincenzo Maurino
Publication date
01-12-2020
Publisher
Springer Berlin Heidelberg
Published in
Graefe's Archive for Clinical and Experimental Ophthalmology / Issue 12/2020
Print ISSN: 0721-832X
Electronic ISSN: 1435-702X
DOI
https://doi.org/10.1007/s00417-020-04915-1

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