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Published in: Pediatric Surgery International 12/2017

01-12-2017 | Review Article

Biliary atresia: unity in diversity

Author: Claus Petersen

Published in: Pediatric Surgery International | Issue 12/2017

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Abstract

Biliary atresia (BA) is a rare disease of unknown origin and unsatisfying outcome. Single, multicenter and national evaluations of epidemiological and outcome data on BA have been periodically published over the course of decades. However, the diversity of the registered parameters and outcome measures impede comparability and cumulative analysis of these very worthwhile studies. Taking into account the fact that BA is a good example of translational research and transition of patients from pediatric surgery and hepatology to transplant surgery and hepatology in general, the interdisciplinary community should make every effort to develop a common platform upon which further activities are conducted. Extending this topic to BA-related diseases might increase the acceptance of research studies and enhance the effectiveness of any recommendations outlined therein. The use of the Internet-based communication platform and registry on http://​www.​bard-online.​com represents the first step in this direction, and the database should be viewed as a helpful tool that guides further activities.
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Metadata
Title
Biliary atresia: unity in diversity
Author
Claus Petersen
Publication date
01-12-2017
Publisher
Springer Berlin Heidelberg
Published in
Pediatric Surgery International / Issue 12/2017
Print ISSN: 0179-0358
Electronic ISSN: 1437-9813
DOI
https://doi.org/10.1007/s00383-017-4156-6

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