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Published in: Pediatric Surgery International 7/2013

01-07-2013 | Original Article

Cloacal malformation variants in male

Authors: Tahmina Banu, Tanvir K. Chowdhury, Mozammel Hoque, M. A. Mushfiqur Rahman

Published in: Pediatric Surgery International | Issue 7/2013

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Abstract

Objective

The published surgical literatures have referred only to females as having cloacal defects and the incidence in males is not well established. As during embryogenesis, both sexes have to pass through the stage of a cloaca, there is every chance of development of cloacal anomalies in males also. Here, we are presenting our experience of male cloacal malformations.

Methods

We identified four cases of male cloaca by reviewing medical records of all anorectal malformation (ARM) patients treated at our institution in the past 19 years. Time of presentation, clinical, radiological, cystoscopic and operative findings, and outcomes were analysed.

Results

Out of 1,837 patients, we identified four cases (0.2 %) of male cloacal variants. All presented after 45 days (range 46 days to 28 years). Three of them had proximal hypospadias, two had a vaginal remnant and cystoscopic evaluation showed the length of the common channel ranged from 0.5 to 8 cm. One patient died of multiple anomalies and the other patients are doing well following reconstruction.

Conclusion

None of the male cloacal patients presented in the neonatal period, proximal hypospadias was the common external genital abnormality and half of them had a vagina. Surgical outcome was satisfactory. The scarcity of reported cases of this group is a subject of further research.
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Metadata
Title
Cloacal malformation variants in male
Authors
Tahmina Banu
Tanvir K. Chowdhury
Mozammel Hoque
M. A. Mushfiqur Rahman
Publication date
01-07-2013
Publisher
Springer-Verlag
Published in
Pediatric Surgery International / Issue 7/2013
Print ISSN: 0179-0358
Electronic ISSN: 1437-9813
DOI
https://doi.org/10.1007/s00383-013-3322-8

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