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Published in: Child's Nervous System 10/2019

01-10-2019 | Syringomyelia | Special Annual Issue

Chiari 1 malformation management: the Red Cross War Memorial Hospital approach

Authors: J. M. N. Enslin, A. G. Fieggen, A. Figaji

Published in: Child's Nervous System | Issue 10/2019

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Abstract

Purpose

In this paper, we aimed to review our institutional opinions and experience with Chiari 1 malformation management to determine physician practice and outcomes.

Methods

Discussion between 3 clinicians about practice preferences and the management of Chiari 1 worldwide. Retrospective review of clinical cases over a 10-year period (2009–2018).

Results

Although there are some minor differences between clinicians in our practice, our approach is broadly similar. We treat incidental Chiari 1 malformations conservatively, with clinical and radiological surveillance, reserving intervention for patients who develop clinical signs or radiological deterioration. We prefer surgical intervention for patients with typical symptoms or a Chiari 1 malformation with radiological progression. If symptoms are atypical, we prefer surveillance. Our preferred operation is a conservative suboccipital craniectomy with expansion duraplasty and adhesiolysis. Our operative complication rate was low and there was no mortality or major morbidity in our series. Surveillance for incidentally discovered Chiari 1 malformations has been a safe practice in our experience.

Conclusion

Clinical practice among three clinicians in our institution is broadly consistent. We have a conservative approach to Chiari 1 malformation management and our approach appears to have a low morbidity.
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Metadata
Title
Chiari 1 malformation management: the Red Cross War Memorial Hospital approach
Authors
J. M. N. Enslin
A. G. Fieggen
A. Figaji
Publication date
01-10-2019
Publisher
Springer Berlin Heidelberg
Published in
Child's Nervous System / Issue 10/2019
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI
https://doi.org/10.1007/s00381-019-04281-2

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