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Published in: Child's Nervous System 2/2017

01-02-2017 | Case Report

Neck swelling due to skull base (pseudo)meningocele protruding through a congenital skull base bone defect: a case report

Authors: Rajeev Sharma, Bhoopendra Singh, Shweta Kedia, Rajinder Kumar Laythalling

Published in: Child's Nervous System | Issue 2/2017

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Abstract

Background

Meningocele is defined as a protrusion of the meninges through an opening in the skull or spinal column, forming a bulge or sac filled with cerebrospinal fluid. A pseudomeningocele is defined as a cerebrospinal fluid (CSF) collection formed due to escape of CSF through a dural defect with trapping of CSF into the surrounding soft tissues. We herby report rare occurrence of a large (pseudo)meningocele in a young patient with congenital skull base defect presenting as upper lateral neck swelling.

Case presentation

We present the case of a 17-year-old boy who had painless progressive swelling right side of the upper neck without any history of meningitis or CSF leak. He had a history of undergoing cranioplasty using steel plates for nontraumatic boggy swelling right parieto-occipital region at the age of 5 years at another hospital. Clinical examination showed painless swelling right side of the upper neck, with positive cough impulse and transillumination. CT head with cisternography showed a large right skull base defect through which a large pseudomeningocele was herniating, thus producing upper neck swelling and compressing oral cavity. The neck swelling and intraoral bulge reduced in size after the coperitoneal shunt.

Conclusion

Differential diagnosis of (pseudo)meningocele should be considered while evaluating a painless progressive upper neck swelling having cough impulse and transillumination in a young patient.
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Metadata
Title
Neck swelling due to skull base (pseudo)meningocele protruding through a congenital skull base bone defect: a case report
Authors
Rajeev Sharma
Bhoopendra Singh
Shweta Kedia
Rajinder Kumar Laythalling
Publication date
01-02-2017
Publisher
Springer Berlin Heidelberg
Published in
Child's Nervous System / Issue 2/2017
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI
https://doi.org/10.1007/s00381-016-3256-2

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