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Child's Nervous System
Published in: Child's Nervous System 10/2011

01-10-2011 | Special Annual Issue

Cloverleaf skull deformity and hydrocephalus

Authors: Guilherme Machado, Federico Di Rocco, Christian Sainte-Rose, Philippe Meyer, Daniel Marchac, Gaëlle Macquet-Nouvion, Eric Arnaud, Dominique Renier

Published in: Child's Nervous System | Issue 10/2011

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Abstract

Objective

This article describes the clinical aspects for both operated and non-operated patients with a cloverleaf skull deformity treated in our service, focusing on hydrocephalus.

Methods

We describe 13 cases of cloverleaf skull deformity treated in our services between 1977 and 2008. Among them, ten were operated (9 out of 13 for the craniofacial stenosis and 7 out of 13 for hydrocephalus).

Results

Hydrocephalus was present in all patients with bilateral lambdoid stenosis. There was no case of hydrocephalus among the patients with unilateral or absent lambdoid stenosis. Associated malformations and severe faciostenosis were associated with higher mortality and morbidity.

Conclusion

The development of hydrocephalus seems to be closely related to a bilateral lambdoid stenosis. The optimal treatment must be tailored individually considering the degree of the malformation and the presence of complications and comorbidities.
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Metadata
Title
Cloverleaf skull deformity and hydrocephalus
Authors
Guilherme Machado
Federico Di Rocco
Christian Sainte-Rose
Philippe Meyer
Daniel Marchac
Gaëlle Macquet-Nouvion
Eric Arnaud
Dominique Renier
Publication date
01-10-2011
Publisher
Springer-Verlag
Published in
Child's Nervous System / Issue 10/2011
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI
https://doi.org/10.1007/s00381-011-1508-8

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