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World Journal of Surgery
Published in: World Journal of Surgery 2/2015

01-02-2015 | Scientific Review

What is the Incidence of Biliary Carcinoma in Choledochal Cysts, When Do They Develop, and How Should it Affect Management?

Authors: Amit V. Sastry, Benjamin Abbadessa, Michael G. Wayne, Justin G. Steele, Avram M. Cooperman

Published in: World Journal of Surgery | Issue 2/2015

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Abstract

The incidence of cancer in choledochal cysts (CCs) in adults was calculated to determine the timing and need for surgery. In 78 publications (1996–2010), 434 of 5780 reported CCs patients had cancer. Cholangiocarcinoma (70.4 %) and gallbladder cancer (23.5 %) were the most common malignancies. Only nine malignancies were reported before age 18 (0.42 %). In contrast, the incidence of malignancy in adults was 11.4 %. The median age for diagnosis of cancer was 42 years, and the incidence increased with each decade.
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Metadata
Title
What is the Incidence of Biliary Carcinoma in Choledochal Cysts, When Do They Develop, and How Should it Affect Management?
Authors
Amit V. Sastry
Benjamin Abbadessa
Michael G. Wayne
Justin G. Steele
Avram M. Cooperman
Publication date
01-02-2015
Publisher
Springer US
Published in
World Journal of Surgery / Issue 2/2015
Print ISSN: 0364-2313
Electronic ISSN: 1432-2323
DOI
https://doi.org/10.1007/s00268-014-2831-5

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