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Abdominal Radiology
Published in: Abdominal Radiology 4/2013

01-08-2013

Bilateral renal lymphangiomatosis: imaging and histopathologic findings

Authors: R. Karkouche, L. Rocher, C. Guettier, G. Corcos, G. Benoît, H. Fernandez, S. Ferlicot

Published in: Abdominal Radiology | Issue 4/2013

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Abstract

Renal lymphangiomatosis is an extremely rare disease characterized by developmental malformation of the lymphatic system surrounding the kidneys. We present the case of a 22-year-old pregnant female discovered because of worsening. Ultrasound, computed tomography, and magnetic resonance imaging studies were performed. An 18 × 11 × 10 cm voluminous cystic subcapsular lesion compressing the left kidney and subcapsular cysts of the right kidney were found. After the delivery, marsupialization was performed and the pathological analysis confirmed the diagnosis of lymphangiomatosis. A review of the literature is proposed.
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Metadata
Title
Bilateral renal lymphangiomatosis: imaging and histopathologic findings
Authors
R. Karkouche
L. Rocher
C. Guettier
G. Corcos
G. Benoît
H. Fernandez
S. Ferlicot
Publication date
01-08-2013
Publisher
Springer US
Published in
Abdominal Radiology / Issue 4/2013
Print ISSN: 2366-004X
Electronic ISSN: 2366-0058
DOI
https://doi.org/10.1007/s00261-012-9977-0

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