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Skeletal Radiology
Published in: Skeletal Radiology 9/2019

01-09-2019 | Osteoarthrosis | Review Article

Progressive pseudorheumatoid dysplasia: a report of three cases and a review of radiographic and magnetic resonance imaging findings

Authors: Christy B. Pomeranz, Janet R. Reid

Published in: Skeletal Radiology | Issue 9/2019

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Abstract

Progressive pseudorheumatoid dysplasia (PPD) is a rare disorder of postnatal skeletal and cartilage development that often presents with similar clinical findings to juvenile idiopathic arthritis. Patients with PPD display findings of progressive cartilage loss and secondary osteoarthritis over serial imaging studies and have an absence of elevation of inflammatory markers. Awareness of the imaging features of PPD on radiographs and magnetic resonance imaging (MRI) may be important for early diagnosis and surveillance of the disease.
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Metadata
Title
Progressive pseudorheumatoid dysplasia: a report of three cases and a review of radiographic and magnetic resonance imaging findings
Authors
Christy B. Pomeranz
Janet R. Reid
Publication date
01-09-2019
Publisher
Springer Berlin Heidelberg
Published in
Skeletal Radiology / Issue 9/2019
Print ISSN: 0364-2348
Electronic ISSN: 1432-2161
DOI
https://doi.org/10.1007/s00256-019-3165-z

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