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01-01-2011 | Review

Update on congenital nephrotic syndromes and the contribution of US

Authors: E. Fred Avni, Kate Vandenhoute, Arnaud Devriendt, Khalid Ismaili, Maxime Hackx, Francoise Janssen, Michelle Hall

Published in: Pediatric Radiology | Issue 1/2011

Abstract

The clinical classification of nephrotic syndrome (NS) is based on age at presentation. However, this classification is arbitrary because the majority of early onset NS has a genetic origin and has a widespread age of onset (from fetal life to several years). The aims of this review are to illustrate the knowledge accumulated on congenital nephrotic syndrome (CNS) in terms of genetics, classification, findings at histology and US–based on a review of the literature.

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Title: Update on congenital nephrotic syndromes and the contribution of US
Authors: E. Fred Avni
Kate Vandenhoute
Arnaud Devriendt
Khalid Ismaili
Maxime Hackx
Francoise Janssen
Michelle Hall
Publication date: 01-01-2011
Publisher: Springer-Verlag
Published in: Pediatric Radiology / Issue 1/2011
Print ISSN: 0301-0449
Electronic ISSN: 1432-1998
DOI: https://doi.org/10.1007/s00247-010-1793-5

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Update on congenital nephrotic syndromes and the contribution of US

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