Published in:
01-12-2013 | Case Report
Hypoplastic Left Heart Syndrome and Pulmonary Veno-occlusive Disease in an Infant
Published in: Pediatric Cardiology | Issue 8/2013
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This report describes an infant with heterotaxy syndrome and severe hypoplasia of the left heart who presented with profound cyanosis at birth despite a large patent ductus arteriosus. Pulmonary venous return was difficult to demonstrate by echocardiography. Angiography showed total anomalous pulmonary venous return via a plexus that drained through the paravertebral veins and bilateral superior vena cavae. Autopsy confirmed these findings, and histopathology demonstrated severe occlusive changes within the pulmonary veins.