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Published in: Pediatric Cardiology 4/2006

01-08-2006

Coexistence of Three Rare Congenital Heart Defects in a Single Patient

A Unique Case with Important Embryologic Implications

Authors: Jonathan Rhodes, Emile A. Bacha, Robet L. Geggel

Published in: Pediatric Cardiology | Issue 4/2006

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Abstract

The unique anatomy, physiology, and surgical repair of a patient with features of three rare congenital heart defects (total anomalous pulmonary venous return to the coronary sinus, cor triatriatum, and unroofed coronary sinus with persistent left superior vena cava to the left atrium) is described. Analysis of this case suggests that these three conditions are linked in that they all may result as a consequence of a defect in the same embryologic process (i.e., incorporation of the pulmonary venous confluence into the left atrium).
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Metadata
Title
Coexistence of Three Rare Congenital Heart Defects in a Single Patient
A Unique Case with Important Embryologic Implications
Authors
Jonathan Rhodes
Emile A. Bacha
Robet L. Geggel
Publication date
01-08-2006
Publisher
Springer-Verlag
Published in
Pediatric Cardiology / Issue 4/2006
Print ISSN: 0172-0643
Electronic ISSN: 1432-1971
DOI
https://doi.org/10.1007/s00246-006-1275-6

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