Published in:
01-04-2006
Giant Atria in Children with Endomyocardial Fibrosis
Published in: Pediatric Cardiology | Issue 2/2006
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We report two cases of endomyocardial fibrosis. The first was a 10-year-old girl with left endocardial ventricular thickening and massive mitral valvular incompetence. Chest x-ray (Fig. 1) showed a severe cardiomegaly secondary to a giant left atrium. She was operated on with excision of the fibrotic endocardium, mitral valvuloplasty, and atrial reduction. The second case was a 12-year-old boy with a fibrous right ventricle totally reduced at its infundibulum and an aneurysmal right atrium. Chest x-ray and apical four-chamber echocardiography show a massively enlarged and disorganized-appearing right atrium (Fig. 2).
Fig. 1
Chest x-ray showing severe enlargement of the left atrium secondary to left ventricular involvement, with severe mitral regurgitation.
Fig. 2
(A) Chest x-ray showing right atrial contour on the right heart border increased in convexity on the chest x-ray. (B) Two-dimensional echocardiogram (apical four-chamber view) demonstrates the totally disorganized architecture of the right heart. The left atrium (LA) and left ventricle (LV) are completely compressed by the right atrium (RA) with marked spontaneous contrast. MV, mitral valve; PE, pericardial effusion; RV, right ventricle.
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