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Pediatric Cardiology
Published in: Pediatric Cardiology 4/2005

01-08-2005

Portosystemic Shunt with Polysplenia and Hypoplastic Left Heart Syndrome

Authors: H. Ikeda, H. Aotsuka, H. Nakajima, M. Sawada

Published in: Pediatric Cardiology | Issue 4/2005

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Abstract

We report a unique case of portosystemic shunt with polysplenia and hypoplastic left heart syndrome. The abnormal vessel connected the right renal vein and the splenic vein. The shunt flow was from the systemic vein to the portal vein before the Fontan-type operation, but it reversed and ran from portal vein to systemic vein after the Fontan-type operation.
Literature
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Kamata, S, Kitayama, Y, Usui, N,  et al. 2000Patent ductus venosus with a hypoplastic intrahepatic portal system presenting intrapulmonary shunt: a case report with banding of the ductus venosusJ Pediatr Surg35655657PubMed
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Kerlan, RK,Jr, Sollenberger, RD, Palubinskas, AJ,  et al. 1982Portal-systemic encephalopathy due to a congenital portocaval shuntAm J Roentgenol13910131015
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Murray, CJ, Yoo, S, Babyn, PS 2003Congenital extrahepatic portosystemic shuntsPediatr Radiol33614620PubMed
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Ono, H, Mawatari, H, Mizoguchi, N, Eguchi, T, Sakura, N 1998Clinical features and outcome of eight infants with intrahepatic porto-venous shunts detected in neonatal screening for galactosemiaActa Paediatr87631634PubMed
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Papagiannis, J, Kanter, RJ, Effman, EL,  et al. 1993Polysplenia with pulmonary arteriovenous malformationsPediatric Cardiol14127129CrossRef
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Peoples, WM, Moller, JH, Edwards, JE 1983Polysplenia: a review of 146 casesPediatric Cardiol4129137
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Sadler, TW 2004Langman's Medical Embryology9Lippincott Williams & WilkinsBaltimore261265
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Uchino, T, Matsuda, I, Endo, F 1999The long-term prognosis of congenital portosystemic venous shuntJ Pediatr135254256PubMed
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Metadata
Title
Portosystemic Shunt with Polysplenia and Hypoplastic Left Heart Syndrome
Authors
H. Ikeda
H. Aotsuka
H. Nakajima
M. Sawada
Publication date
01-08-2005
Publisher
Springer-Verlag
Published in
Pediatric Cardiology / Issue 4/2005
Print ISSN: 0172-0643
Electronic ISSN: 1432-1971
DOI
https://doi.org/10.1007/s00246-004-0737-y

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